Children with operated metopic synostosis performed significantly worse on measures of motor functioning (g w = −.45), visuospatial skills (g w = −.32), attention (g w = −.50), executive functioning (g w = −.36), arithmetic ability (g w = −.37), and behavior (g w = −.34). The records of 36 consecutive children with metopic synostosis followed at one craniofacial center from 1978 to 1993 were reviewed and parental questionnaires were completed to establish the frequency of mental retardation, learning disabilities, and behavioral problems associated with this synostosis. 19(9):1678-89. . The use of sagittal springs with strip craniectomy may be recommended for sagittal synostosis if the child is younger than 5 months at the time of initial surgery. Hum Mol Genet. ... Study how the condition affects learning and behavior; ... Fronto-orbital surgery for metopic and unilateral coronal synostosis. This page from Great Ormond Street Hospital (GOSH) explains the causes, symptoms and treatment of metopic craniosynostosis (also … Craniosynostosis is when one or more of the special seams (sutures) in a baby's skull close earlier than normal. Children with metopic, unicoronal and lambdoid synostosis tended to score lower on most measures than those with sagittal fusion (P<.001 to .82). Metopic craniosynostosis. Surgical therapy for true metopic synostosis involves a fronto-orbital advancement which allows for widening the skull at the temporal fossa. Also known as cranial spring surgery. This corrects the abnormal triangular shape of the forehead and increases the intracranial space in the anterior fossa. Treatment involves releasing the suture and expanding and rounding out the upper face, forehead and skull. 2010 May 1. Miraoui H, Ringe J, Haupl T, Marie PJ. Increased EFG- and PDGFalpha-receptor signaling by mutant FGF-receptor 2 contributes to osteoblast dysfunction in Apert craniosynostosis. The metopic suture begins at the nose and continues superiorly to meet the sagittal suture. J Craniofac Surg. Metopic synostosis is presently the second most common form of craniosynostosis, accounting for 19% to 28% of cases 53–55 and having a prevalence of 0.9 to 2.3 per 10 000 live births. 2009 Sep. 20(5):1439-44. . Children with metopic, unicoronal or lambdoid synostosis were much more likely to have a learning problem than children with the most common form of single-suture craniosynostosis – sagittal synostosis. Metopic craniosynostosis is a type of non-syndromic craniosynostosis that occurs when the metopic suture fuses before birth. This type affects the metopic suture, which runs from the top of the head down the middle of the forehead to the bridge of the nose. 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